Primary mesenchymal chondrosarcoma of the lung
Primary mesenchymal chondrosarcoma of the lung
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DOI：
10.1016/s0003-4975(01)03462-2
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发表时间：
2002-06-01
影响因子：
4.6
通讯作者：
Huang, SC
中科院分区：
文献类型：
--
作者：
Huang, HY;Hsieh, MJ;Huang, SC
间充质软骨肉瘤已在体细胞软组织和骨骼中得到了充分的证明。这是一种罕见的软骨肉瘤亚型，其特征是存在软骨样岛或较少的骨样组织包裹在致密的原始小蓝色间充质细胞层中，并伴有血管外皮细胞瘤样血管，或两者兼而有之。绝大多数先前发表的肺间充质软骨肉瘤是转移性的。据我们所知，文献中只报道了一例原发性肺间充质软骨肉瘤。在此，我们报告第二例原发性肺间充质软骨肉瘤，并强调活检可能只产生非特异性的小蓝色细胞，而对切除标本的详细评估可以明确诊断这种罕见的肺肿瘤。
Mesenchymal chondrosarcoma has been well documented in the somatic soft tissue and bone. It is a rare subtype of chondrosarcoma characterized by the presence of islands of chondroid or by less osteoid tissue enmeshed within dense sheets of primitive small blue mesenchymal cells with hemangiopericytoma-like vessels, or by both. The vast majority of previously published pulmonary mesenchymal chondrosarcoma was metastatic. To the best of our knowledge, only one case of primary pulmonary mesenchymal chondrosarcoma has been described in the literature. Herein, we report the second case of primary mesenchymal chondrosarcoma of the lung and emphasize that biopsy may yield only nonspecific small blue cells, whereas a detailed evaluation of the resected specimen allows definite diagnosis of this rare lung tumor.