Consequences of Delayed Dental Extraction in Lesch-Nyhan Disease.
Consequences of Delayed Dental Extraction in Lesch-Nyhan Disease.
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DOI：
10.1002/mdc3.12040
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发表时间：
2014-09
影响因子：
4
通讯作者：
Jinnah, H A
中科院分区：
文献类型：
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作者：
Goodman, Emily M;Torres, Rosa J;Puig, Juan G;Jinnah, H A
莱希-尼汉病（LND）患者经常从事自残性咬伤。这个问题需要艰难的管理选择，有时包括拔除牙齿。尽管许多卫生保健专业人员不愿意为儿童拔牙，因为无牙状态会对美容造成永久性的负面影响，但自咬造成的面部和舌头毁容可能更糟。我们分析了5例使用护齿器保护牙齿的LND患者的记录。成功与否各不相同，最终有4例需要拔牙。我们也回顾了以前发表的关于使用牙齿装置在LND中保留牙齿的病例。已经推荐了各种各样的设备，但失败率很高，并且仍然经常需要拔牙。虽然不是在所有情况下都需要拔牙，但当咬伤严重时，不应该推迟拔牙。
Patients with Lesch-Nyhan disease (LND) often engage in self-injurious biting. This problem requires difficult management choices, sometimes including removal of the teeth. Although many health care professionals are reluctant to remove teeth in a child because of the permanent negative cosmetic consequences of the edentulous state, disfigurement of the face and tongue from self-biting can be worse. We analyzed the records of 5 LND patients who used mouth guards to spare the teeth. Success was variable, and dental extraction ultimately was required in 4 cases. We also reviewed previously published cases on the use of dental devices to spare teeth in LND. Various devices have been recommended, but failure rates are high, and tooth extraction often is still needed. Although dental extraction is not required in all cases, it should not be delayed when biting is severe.