Synovial sarcoma of kidney in a child: A rare presentation.
Synovial sarcoma of kidney in a child: A rare presentation.
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DOI：
10.4103/0971-9261.172502
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发表时间：
2016-04
影响因子：
--
通讯作者：
Sagar T
中科院分区：
文献类型：
--
作者：
Radhakrishnan V;Dhanushkodi M;Narayanswamy K;Raja A;Sundersingh S;Sagar T
在文献中没有报道过小儿原发性肾滑膜肉瘤的病例。肾滑膜肉瘤的治疗是从其他部位软组织肉瘤的治疗中推断出来的。我们报告一位四岁的女性，她被怀疑患有威尔姆斯瘤。由于对Wilms肿瘤的新辅助化疗没有反应，患者接受了引导活检。活检符合原发性肾滑膜肉瘤。患儿接受了新辅助化疗方案的改变和手术治疗。通过聚合酶链反应证实t （X, 18）易位，证实滑膜肉瘤的诊断。
There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms’ tumor. The patient underwent guided biopsy as she did not respond to neoadjuvant chemotherapy for Wilms’ tumor. The biopsy was consistent with primary renal synovial sarcoma. The child was treated with change in her neoadjuvant chemotherapy regimen and surgery. The diagnosis of synovial sarcoma was confirmed by demonstrating the t (X, 18) translocation using polymerase chain reaction.