Hypoplastic Left Heart Syndrome: An Overview for Primary Care Providers
Hypoplastic Left Heart Syndrome: An Overview for Primary Care Providers
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DOI：
10.1542/pir.2018-0005
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发表时间：
2019-07-01
影响因子：
1.3
通讯作者：
Qureshi, Muhammad Yasir
中科院分区：
文献类型：
--
作者：
Javed, Rabia;Cetta, Frank;Qureshi, Muhammad Yasir
左心发育不良综合征是最复杂的先天性心脏病之一，需要多次心脏手术才能生存。诊断通常在产前或出生后不久确定。手术的每个阶段都有独特的血流动力学情况，需要更深入的了解来管理常见的儿科问题，如脱水和呼吸道感染。仔细的多学科参与这些复杂患者的护理正在改善他们的结果，但是，发病率和死亡率仍然很高。在这篇综述中，我们重点介绍了初级保健提供者应该知道的各种手术阶段的血流动力学方面，以管理这些具有挑战性的患者。
Hypoplastic left heart syndrome is one of the most complex congenital heart diseases and requires several cardiac surgeries for survival. The diagnosis is usually established prenatally or shortly after birth. Each stage of surgery poses a unique hemodynamic situation that requires deeper understanding to manage common pediatric problems such as dehydration and respiratory infections. Careful multidisciplinary involvement in the care of these complex patients is improving their outcome; however, morbidity and mortality are still substantial. In this review, we focus on the hemodynamic aspects of various surgical stages that a primary care provider should know to manage these challenging patients.