Well-differentiated papillary adenocarcinoma arising in a supratentorial enterogenous cyst: Case report
Well-differentiated papillary adenocarcinoma arising in a supratentorial enterogenous cyst: Case report
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DOI：
10.1097/00006123-199812000-00131
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发表时间：
1998-12-01
期刊：
影响因子：
4.8
通讯作者：
Tihan, T
中科院分区：
文献类型：
--
作者：
Ho, LC;Olivi, A;Tihan, T
目的和重要性：我们报告一例发生于幕上肠源性囊肿的高分化乳头状腺癌。本文介绍了这一病例的临床病理特征并简要回顾了文献。临床表现：一名45岁女性，突然出现感觉性癫痫发作，左侧面部、左腿和左臂感觉异常。最初的临床印象是一个转移性病变，和全面的转移性workup显示没有证据表明肿瘤elsearch.INTERVENTION：一个整体切除的实性囊性肿瘤额顶骨开颅手术。初次手术后16个月，患者出现颅内压升高和巨大顶叶囊肿的体征。在第二次开颅手术的时候，囊肿被开窗。结论：初步手术材料的病理研究显示，它是一个分化良好的乳头状腺癌与肠源性囊肿。第二个手术标本仅由良性囊肿壁组成。患者从第二次手术中顺利恢复，术后6个月无症状。重要的是认识到罕见的可能性恶性进展的良性肠源性囊肿在中枢神经系统进行了讨论。
OBJECTIVE AND IMPORTANCE: We report a case of a well-differentiated papillary adenocarcinoma arising in an supratentorial enterogenous cyst. The clinicopathological features of this case and a brief review of the literature are presented,CLINICAL PRESENTATION: A 45-year-old woman presented with abrupt onset of sensory seizures and abnormal sensation on the left side of her face, left leg, and left arm. Radiological studies showed a cystic extraaxial tumor with mass effect in the right parietal area. The initial clinical impression was a metastatic lesion, and a comprehensive metastatic workup revealed no evidence of tumor elsewhere.INTERVENTION: A gross total resection of the solid cystic tumor was achieved by a frontoparietal craniotomy. Sixteen months after the initial surgery, the patient presented with signs of increased intracranial pressure and a large parietal cyst. The cyst was fenestrated at the time of the second craniotomy.CONCLUSION: A pathological study of the initial surgical material revealed it to be a well-differentiated papillary adenocarcinoma in association with an enterogenous cyst. The second surgical specimen consisted only of the benign cyst wall. The patient recovered uneventfully from the second surgery and was free of symptoms 6 months postoperatively. The importance of recognizing the rare possibility of malignant progression of a benign enterogenous cyst in the central nervous system is discussed.