Cochlear implantation in a patient with superficial siderosis
Cochlear implantation in a patient with superficial siderosis
复制标题
DOI：
10.1016/j.anl.2011.10.009
复制
发表时间：
2012-12-01
影响因子：
1.7
通讯作者：
Yoshizaki, Tomokazu
中科院分区：
文献类型：
--
作者：
Sugimoto, Hisashi;Ito, Makoto;Yoshizaki, Tomokazu
摘要浅表性铁质沈积症是一种罕见的疾病，其特徴为含铁血黄素在软脑膜、软膜下组织、脊髓及脑神经的累积。第一个临床病理描述是在1908年报道的。大多数患者（95%）在病程早期出现进行性双侧听力损失。对于继发于浅表性铁质沉着症的听力损失患者，最初的治疗包括使用助听器进行声音放大。但是，在患者无法从助听器中获得显著益处的情况下，可以考虑人工耳蜗植入。只有10项研究描述了在浅表铁质沉着症中使用人工耳蜗植入物，结果各不相同。我们报告一位65岁的女性，因浅表性铁质沉着症而导致双侧进行性感音神经性听力损失，她从人工耳蜗植入术中获益匪浅。(C)2011爱思唯尔爱尔兰有限公司保留所有权利。
Superficial siderosis is a rare disease characterized by accumulation of hemosiderin in the leptomeninges, subpial tissue, spinal cord, and cranial nerves. The first clinicopathological description was reported in 1908. Most patients (95%) experience progressive bilateral hearing loss that begins early in the course of disease. The initial management of a patient with hearing loss secondary to superficial siderosis involves sound amplification using hearing aids. However, cochlear implants can be considered in cases where the patient can no longer gain significant benefit from hearing aids. Only 10 studies have described the use of cochlear implants in superficial siderosis and results have been variable. We report the case of a 65-year-old woman with bilateral progressive sensorineural hearing loss caused by superficial siderosis who benefited significantly from cochlear implantation. (C) 2011 Elsevier Ireland Ltd. All rights reserved.