Radiologic findings of hamartomas of the tuber cinereum and hypothalamus.
Radiologic findings of hamartomas of the tuber cinereum and hypothalamus.
复制标题
灰结节和下丘脑错构瘤的放射学表现。
作者：
S. R. Lin;M. Bryson;R. Gobien;C. Fitz;Y. Y. Lee
报道了5例，其中4例经组织学证实，或儿童（年龄范围：2--12岁）灰结节和下丘脑错构瘤。 3 例患有早发性青春期，所有这些病例的错构瘤均位于视交叉和脑桥之间的基底池，具有典型的灰块茎错构瘤的领扣形状和大小。第三例表现为头痛，鞍上区有一个巨大的钙化肿块，最初被认为是颅咽管瘤。第四例患者下丘脑实质内有错构瘤，并表现为低钠血症和颞叶癫痫发作。
Five cases, four histologically proved, or hamartoma of the tuber cinereum and hypothalamus in children (age range: 2--12 years) are reported. Three cases had pubertas praecox, and in all of these the hamartoma was located in the basal cistern between the chiasm and pons, and had a collar button shape and size typical of hamartoma of the tuber cinereum. In the third case, which presented with headache, a huge calcified mass in the suprasellar region was initially thought to be craniopharyngioma. The fourth case had a hamartoma within the substance of the hypothalamus and presented with hyponatremia and temporal lobe seizures.