THE MOTOR UNIT IN MUSCULAR-DYSTROPHY, A SINGLE FIBER EMG AND SCANNING EMG STUDY
THE MOTOR UNIT IN MUSCULAR-DYSTROPHY, A SINGLE FIBER EMG AND SCANNING EMG STUDY
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DOI：
10.1136/jnnp.46.11.981
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发表时间：
1983-01-01
影响因子：
11
通讯作者：
STALBERG, E
中科院分区：
文献类型：
--
作者：
HILTONBROWN, P;STALBERG, E
营养不良患者的肌肉表现为纤维密度增加，在某些记录中出现异常低的抖动，更常见的是抖动增加。电机单元的横截面具有正常长度。没有异常的容量传导特征的迹象。纤维密度的增加是由于肌肉动作电位发生器数量的局限性增加。这一发现与由于纤维丢失而导致的运动单位重塑以及纤维再生和再神经支配的修复过程是一致的。
Dystrophic muscle in patients shows increase in fiber density, abnormally low jitter in some recordings and more often increased jitter. The cross section of the motor unit has normal length. There are no signs of abnormal volume conduction characteristics. The increased fiber density is due to localized increase in the number of muscle action potential generators. The findings are compatible with a remodeling of the motor unit due to fiber loss and a reparative process with fiber regeneration and reinnervation.