Peculiar inflammatory cutaneous metastasis from stomach adenocarcinoma
Peculiar inflammatory cutaneous metastasis from stomach adenocarcinoma
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胃腺癌的特殊炎症性皮肤转移
DOI：
10.1111/j.1365-2133.1997.tb02179.x
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发表时间：
1997
影响因子：
10.3
通讯作者：
A. Sungur
中科院分区：
文献类型：
--
作者：
S. Şahin;U. Hindioḡlu;M. Benekli;B. Sivri;C. Sökmensüer;A. Sungur
主动脉缩窄和脐上缝是 GFH 患者比正常儿童更常见的其他畸形。'''* 在某些情况下报告了所有这些异常的重叠，并且所有这些异常都可能出现在同一儿童中。在这种情况下，Goh 和 Lo 定义了一种新的 3C 综合征。由于同时存在小脑发育不全。海绵状血管瘤。和主动脉缩窄发生在同一患者身上。 Frieden 等人提出了另一个术语，因为观察到还可能发生更复杂的异常范围。他们提出了缩写词 PHACE 综合征，以表示这种神经皮肤综合征的主要特征： P. 后颅窝畸形： H. 血管瘤； A.动脉异常； C.主动脉缩窄和心脏缺陷； E.眼睛异常。这些作者在描述两个案例并回顾文献后得出了这个缩写词。所有患有这种综合征的患者都存在 GFH：其中 SS% 是女性，就像我们的病例一样。"'"' 74% 的人患有后颅窝脑畸形。 41% 出现动脉异常。 2b% 患有心脏或主动脉畸形，26% 出现不寻常的眼睛异常。”
Aortic coarctation and supraumbilical raphe are other mallbrmations more frequently observed in patients with GFH than in normal children.'"'* Overlapping of all these anomalies has been reported in some instances, and ail may present in the same child. In this context, a new 3C syndrome was defined by Goh and Lo.' as the concurrence of cerebellar hypoplasia. cavernous haemangioma. and aortic coarctation in the same patient. Another term was proposed by Frieden et fl/.r on observing that a more complex range of abnormalities may also occur. They proposed the acronym PHACE syndrome, to denote the major features of this neurocutaneous syndrome: P. posterior fossa malformations: H. haemangiomas; A. arterial abnormalities; C. coarctation of the aorta and cardiac defects; and E. eye abnormalities. These authors arrived at this acronym after describing two cases and reviewing the literature. GFH was present in all patients with this syndrome: SS% of them were females, as in our case."'"' 74% had a brain malformation of the posterior fossa. 41% presented arterial anomalies. 2b% had cardiac or aortic malformations and 26% presented unusual eye abnormalities."