Cystic meningioangiomatosis
Cystic meningioangiomatosis
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DOI：
10.1159/000094071
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发表时间：
2006-01-01
影响因子：
0.7
通讯作者：
Iwasaki, Yoshinobu
中科院分区：
文献类型：
--
作者：
Kobayashi, Hiroyuki;Ishii, Nobuaki;Iwasaki, Yoshinobu
报道了一例伴有罕见囊肿形成的脑膜血管瘤病。一名 14 岁男孩，没有任何 2 型神经纤维瘤病的症状，自 12 岁起出现难治性复杂部分性和全身性癫痫发作。神经放射学研究显示大脑左额叶有异常囊性肿块伴钙化。肿瘤位于软脑膜和大脑皮层。由于苯妥英和丙戊酸钠的药物治疗不足以控制癫痫发作，该患者接受了手术治疗。术中皮质电图显示，在邻近病变的皮质处记录到癫痫病灶。组织病理学显示脑膜血管瘤病伴脑膜瘤样结节的具体特征。手术后，患者服用抗惊厥药物后未出现任何癫痫发作。将脑膜血管瘤病与其他可能的皮质病变区分开来很重要，并且在切除前应仔细考虑癫痫病灶，因为它是癫痫发作的良性且可通过手术控制的原因。版权所有 (c) 2006 S. Karger AG，巴塞尔。
A case of cerebral meningioangiomatosis with rare cyst formation is reported. A 14-year-old boy without any stigmata of neurofibromatosis type 2 presented intractable complex partial and generalized seizures since the age of 12 years. Neuroradiological studies showed an abnormal cystic mass with calcification in the left frontal lobe of the cerebrum. The tumor was located in the leptomeninges and cerebral cortex. The patient underwent surgical treatment because medical treatment with phenytoin and sodium valproate was not sufficient to control the seizures. An intraoperative electrocorticogram revealed that epileptic foci were recorded from the cortex, which was adjacent to the lesion. Histopathology showed specific features of meningioangiomatosis with meningioma-like nodules. The patient did not have any seizures with anticonvulsants after surgery. It is important to distinguish meningioangiomatosis from other possible cortical lesions and epileptic foci should be carefully considered before resection, because it is a benign and surgically manageable cause of seizures. Copyright (c) 2006 S. Karger AG, Basel.