Unusual presentation of a first Branchial cleft cyst associated with an abnormal bony canal -a case report-
Unusual presentation of a first Branchial cleft cyst associated with an abnormal bony canal -a case report-
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DOI：
10.1186/s40463-020-00426-5
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发表时间：
2020-05-29
影响因子：
3.4
通讯作者：
Denoyelle, F.
中科院分区：
文献类型：
--
作者：
Fanous, A.;Couloigner, V;Denoyelle, F.
背景：第一鳃裂畸形是罕见的，仅占所有鳃裂畸形的10%。我们报告一个更罕见和独特的情况下，鳃裂囊肿的功能，第一和第二弓derivatives.Case介绍：一个6岁的男孩向我们提出了左传导性听力损失与前鼓室角蛋白碎片和同侧疼痛的颈部肿块。患者既往有2年前因疑似中耳炎进行左耳手术和6个月前左颈脓肿引流的病史。CT和MRI显示病变起源于外耳道，并通过位于面神经内侧的骨管向颈部延伸，终止于咽旁囊肿。在一个手术阶段完成完全切除，包括三个不同的步骤：机器人辅助经口咽囊肿切除术，耳内入路和腮腺切除术。我们相信，我们对这例罕见的第一鳃裂囊肿延伸至咽部的详细描述，可能是第一鳃裂囊肿和第二鳃裂囊肿的混合病例，可以作为一个有价值的工具，耳鼻喉科-头颈外科医生谁遇到了类似的不寻常的介绍。
Background: First branchial cleft anomalies are rare, accounting for only 10% of all branchial cleft anomalies. We report an even more rare and unique case of a branchial cleft cyst with features of both first and second arch derivatives.Case presentation: A 6-year-old boy presented to us with a left conductive hearing loss associated with pre-tympanic keratin debris and an ipsilateral painful cervical mass. He had a past medical history of left ear surgery for presumed cholesteatoma 2 years prior and left neck abscess drainage 6 months prior. CT and MRI revealed a lesion originating in the external auditory canal and extending cervically through a bony canal located medial to the facial nerve and terminating as a parapharyngeal cyst. The complete removal was accomplished in one surgical stage consisting of three distinct steps: robotic assisted transoral resection of the pharyngeal cyst, an endaural approach and a parotidectomy approach.Conclusion: We believe that our detailed description of this rare first branchial cleft cyst with pharyngeal extension, possibly a hybrid case between a first and second branchial cyst, can serve as a valuable tool to Otolaryngologists - Head and Neck Surgeons who come across a similar unusual presentations.