IDIOPATHIC INFLAMMATORY ORBITAL PSEUDOTUMOR IN CHILDHOOD .1. CLINICAL CHARACTERISTICS
IDIOPATHIC INFLAMMATORY ORBITAL PSEUDOTUMOR IN CHILDHOOD .1. CLINICAL CHARACTERISTICS
复制标题
DOI：
10.1001/archopht.1978.03910060164013
复制
发表时间：
1978-01-01
影响因子：
--
通讯作者：
JAKOBIEC, FA
中科院分区：
文献类型：
--
作者：
MOTTOW, LS;JAKOBIEC, FA
对29例年龄在20岁以下的眼眶炎性假瘤患者的临床资料进行了回顾分析。没有性取向，尽管左眼眶受累的频率是右眼眶的两倍。患者通常有突然发作的眼周疼痛、清晨肿胀、肿胀、结膜和眼外肌注射、眼球突出、可触及的肿块和眼外运动障碍。视力通常只在发病时受到轻微影响。在这些患者中，45%的患者在没有明显的系统性疾病的情况下，已经或随后发展为双侧眼眶受累。乳头水肿和虹膜炎的发生率分别为35%和28%，尤其是在双侧病例中。所有病例都对类固醇有反应，但双侧疾病最容易依赖类固醇。永久性功能障碍最常见于交替复发的双侧疾病患者或接受手术探查的患者。
The cases of 29 patients aged 20 yr or less with orbital inflammatory pseudotumor were studied retrospectively. There was no sex predilection, although the left orbit was involved twice as often as the right. Patients typically had abrupt onset of periocular pain, early-morning swelling, chemosis, conjunctival and extraocular muscle injection, proptosis, a palpable mass and extraocular motility disturbances. Visual acuity was usually only mildly affected at onset. Of the patients, 45% had or subsequently developed bilateral orbital involvement in the absence of notable systemic diseases. Papilledema and iritis were seen in 35% and 28% of patients, respectively, particularly in bilateral cases. All cases responded to steroids, but bilateral disease was the most apt to become steroid dependent. Permanent functional impairments were seen most commonly in patients who had alternating recurrent bilateral disease or who underwent surgical exploration.