DYSTROPHIA RETICULARIS LAMINAE PIGMENTOSAE RETINAE
DYSTROPHIA RETICULARIS LAMINAE PIGMENTOSAE RETINAE
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网状营养不良症
DOI：
10.1111/j.1755-3768.1950.tb05361.x
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发表时间：
1950
影响因子：
3.4
通讯作者：
H. Sjögren
中科院分区：
文献类型：
--
作者：
H. Sjögren
2.“)Bodihl A.8岁。第一次出现近视是在9月1日。1946年2月23日。右眼：巩膜位于角膜缘外，与角膜的上颞周相对应，明显变薄，脉络膜穿透，轻微向前凸出；最好描述为开始的间隔性葡萄肿。前房极浅，周边几乎没有前房。在瞳孔区域，房室只剩下一条狭缝。瞳孔大约正常大小，鼻部略微向上拉长。瞳孔反应正常。虹膜组织形态正常。散巩膜透照时，虹膜底部的色素层明显萎缩。在用同种异丙托品扩大瞳孔后，晶状体裸露，只有上鼻部仍被虹膜覆盖。镜片边缘明显是圆形的，所以镜片几乎是球状的。带状纤维清晰可见。视盘正常。无血管脱位，其他方面也正常。中心凹中央可见一个黑点，高倍镜下可见由细小的色素颗粒堆积而成；其他情况下，中心凹是正常的。黄斑反射正常。在颞叶血管之间的区域可观察到清晰的黑色素线网络。(图1)。这些网格是由锐利的
2.”) Bodihl A. Age 8. Presented with myopia the first time on Sept. 23, 1946. Right eye: Sclera immediately outside limbus corresponding to the upper temporal circumference of the cornea, was markedly thin with the choroid showing through, slightly bulging forward; best described as beginning intercalary staphyloma. The anterior chamber was extremely shallow, almost absent in the peripheral portions. In the pupillary area only a narrow slit remained of the chamber. The pupil was of about normal size, slightly elongated upwards nasally. The pupillary reactions were normal. The iris tissue was of normal appearance. On diascleral transillumination the pigmented layer a t the temporal portion of the base of the iris was found to be markedly atrophic. After dilatation of the pupil by means of homatropine, the lens was laid bare, only the upper nasal portion still being covered by the iris. The lens border was distinctly rounded so that the lens was almost globular. The zonular fibres were clearly visible. The optic disc was normal. There was no dislocation of the vessels which were normal also in other respects. In the centre of the fovea was seen a black spot which on high magnification was found to consist of an accumulation of fine pigment-granules; the fovea was otherwise normal. The macular reflexes were normal. A clearly defined network of black pigmented lines was noticed over the area between the temporal vessels. (Fig. 1). The meshes were formed from sharp