Auxiliary Partial Orthotopic Living Donor Liver Transplantation With a Small-for-Size Graft for Congenital Absence of the Portal Vein
Auxiliary Partial Orthotopic Living Donor Liver Transplantation With a Small-for-Size Graft for Congenital Absence of the Portal Vein
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DOI：
10.1002/lt.22179
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发表时间：
2010-12-01
影响因子：
4.6
通讯作者：
Taguchi, Tomoaki
中科院分区：
文献类型：
--
作者：
Matsuura, Toshiharu;Soejima, Yuji;Taguchi, Tomoaki
先天性门静脉缺失（CAPV）合并肝外门静脉系统分流是一种罕见的畸形；完全缺失型，阿伯内西畸形I型，尤其罕见。肝移植治疗I型CAPV是目前公认的唯一治疗方法，但迄今为止报道较少；同时，辅助部分原位肝移植（APOLT）被认为是一种非常有效的选择，特别是对于儿童患者。在这里，我们报告了一名18岁的CAPV，脾功能不全和髂分流血管的成年患者，他使用小尺寸移植成功地进行了APOLT治疗。据我们所知，这是第一例成功应用APOLT治疗CAPV的成人患者。这是一种可行的方法：它不仅满足了成年患者肝脏的代谢需求，而且有可能治愈CAPV。中华肝病杂志，2010(4):1437-1439。(c) 2010年。
Congenital absence of the portal vein (CAPV) with an extrahepatic portosystemic shunt is a rare malformation; the completely absent type, Abernethy malformation type I, is especially rare. Liver transplantation for CAPV type I has been recently recognized as the only curative operation, but few reports have been published so far; meanwhile, auxiliary partial orthotopic liver transplantation (APOLT) has been proposed to be a very effective option, especially for pediatric patients. Here we present an 18-year-old adult patient with CAPV, asplenia, and an iliac shunt vessel who was managed successfully with APOLT using a small-for-size graft. To the best of our knowledge, this is the first adult patient who has experienced success with APOLT for CAPV. This is a feasible procedure: it not only fulfills the metabolic demands of the liver for adult patients but also potentially cures CAPV. Liver Transpl 16:1437-1439, 2010. (C) 2010 AASLD.