Pulmonary sequestration.
Pulmonary sequestration.
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DOI：
10.1016/j.prrv.2003.09.009
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发表时间：
2004-03-01
影响因子：
5.8
通讯作者：
Humphrey, Gillian M E
中科院分区：
文献类型：
--
作者：
Corbett, Harriet J;Humphrey, Gillian M E
肺隔离症是指肺组织的一部分从异常的全身动脉接受血液供应的情况。存在三种主要变异：叶内、叶外和交通性支气管肺前肠畸形。静脉引流通常通过体静脉进行，尽管引流至肺静脉的情况已有充分记录。肺隔离症是第二常见的先天性肺异常。受影响的个体通常有其他异常现象，这些异常现象是与隔离相关的大部分死亡的原因。诊断需要高度怀疑，特别是对于胸部 X 光检查提示存在肿块的儿童、反复胸部感染的儿童以及肺隔离谱中发现其他异常的儿童。尽管在某些情况下，饲管栓塞也有一定作用，但通常建议进行手术切除。
Pulmonary sequestration refers to the situation whereby a portion of lung tissue receives its blood supply from an anomalous systemic artery. Three main variants exist: intralobar, extralobar and communicating bronchopulmonary foregut malformations. Venous drainage is typically via a systemic vein, although drainage into the pulmonary veins is well documented. Pulmonary sequestrations are the second commonest congenital lung anomaly. Affected individuals often have other anomalies which are responsible for most of the mortality associated with sequestrations. Diagnosis requires a high index of suspicion particularly in any child with a chest x-ray suggesting the presence of a mass, those with recurrent chest infections and those with other anomalies seen with the pulmonary sequestration spectrum. Surgical excision is usually advised, although embolisation of the feeding vessel has a role in selected cases.