Molecular pathophysiology and stem cell treatment for mitochondrial diseases: insights from the French Canadian variant of Leigh Syndrome

线粒体疾病的分子病理生理学和干细胞治疗：来自法裔加拿大人利氏综合征变体的见解

• 批准号: 383302
• 负责人: Cuillerier Alexanne
• 金额: $ 7.65万
• 依托单位: University of Ottawa
• 依托单位国家: 加拿大
• 项目类别: Studentship Programs
• 财政年份: 2017
• 资助国家: 加拿大
• 起止时间: 2017-10-01 至 2020-10-01
• 项目状态: 已结题
• 来源: https://webapps.cihr-irsc.gc.ca/decisions/p/project_details.html?applId=383302&lang=en
• 关键词: Bioenergetics; Genetic Mitochondrial Diseases; Leigh Syndrome; Liver; Lrpprc; Mesenchymal Stem Cells; Mitochondria; Mitochondrial Dysfunctions; Physiology; Stem Cell Therapy

Mitochondria are structures within our cells that are responsible, among other things, for the production of energy. Genetic Mitochondrial Diseases affect the proper functioning of mitochondria. Organs with high-energy demand, such as muscles, heart and b

线粒体是我们细胞内的一种结构，除其他外，它负责产生能量。遗传性线粒体疾病影响线粒体的正常功能。需要高能量的器官，如肌肉、心脏和b