BONE CHANGES IN ORBITAL NEUROFIBROMATOSIS.
BONE CHANGES IN ORBITAL NEUROFIBROMATOSIS.
复制标题
眼眶神经纤维瘤病的骨骼变化。
DOI：
--
复制
发表时间：
1963
影响因子：
2.6
通讯作者：
E. H. Burrows
中科院分区：
文献类型：
--
作者：
E. H. Burrows
神经纤维瘤累及眼眶和视觉器官产生独特的（但不是特定的）影像学表现，可能包括先天性蝶骨缺损、骨眼眶过度生长、颞窝膨出、视神经管扩大和垂体窝异常。这种模式在神经纤维瘤病中相当常见，也并不罕见——在59例经证实的x线片患者中有15例出现这种情况。大约10%的视神经胶质瘤发生在神经纤维瘤病患者身上。本文描述了15例患者中12例的临床和放射学特征，并讨论了放射学鉴别诊断。正确的放射学解释的重要性在于防止不必要的开颅手术，因为占位性病变可能被错误地认为是与该疾病相关的放射学特征的原因。
Neurofibromatous involvement of the orbit and visual apparatus produces a distinctive (but not specific) radiological pattern which may include a congenital defect of the sphenoid bone, overgrowth of the bony orbit, a bulging temporal fossa, an enlarged optic canal and an abnormal pituitary fossa. This pattern is fairly constant and not uncommon in neurofibromatosis—it was present in 15 of 59 proven cases whose radiographs were examined. About 10 per cent of all optic gliomata occur in patients with neur-fibromatosis. The clinical and radiological features of 12 of the 15 patients are described and the radiological differential diagnosis discussed. The importance of correct radiological interpretation lies in the prevention of needless craniotomy since a space occupying lesion may mistakenly be thought responsible for the radiological features associated with the condition.