Congenital portosystemic shunts with and without gastrointestinal bleeding - case series
Congenital portosystemic shunts with and without gastrointestinal bleeding - case series
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DOI：
10.1007/s00247-015-3417-6
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发表时间：
2015-12-01
影响因子：
2.3
通讯作者：
Qiao, Zhongwei
中科院分区：
文献类型：
--
作者：
Gong, Ying;Zhu, Hui;Qiao, Zhongwei
先天性门体分流症的临床表现多变，消化道出血是一种少见的表现，本文描述了11例先天性门体分流症的影像学表现，其中6例合并消化道出血，5例不合并消化道出血我们对11例诊断为先天性门体分流的儿童的临床和影像学数据集进行了回顾性研究。其中先天性门体分流7例，肝外门体分流7例，肝内门体分流4例。6例消化道出血患者存在肝外门体分流，影像学结果显示分流起源于脾肠系膜交界处（n = 5）或脾静脉（n = 1）并与髂内静脉相连。在5例无消化道出血的先天性门体分流中，1例为肝外门体分流，4例为肝内门体分流，大多数先天性门体分流合并消化道出血患者的分流是通过肠系膜下静脉将门静脉血引流至髂静脉。这种类型的分流术并不常见，但这种类型的分流术的胃肠道出血的伴随发生率很高。
The clinical presentation of congenital portosystemic shunt is variable and gastrointestinal bleeding is an uncommon presentation.To describe the imaging features of congenital portosystemic shunt as it presented in 11 children with (n = 6) and without gastrointestinal bleeding (n = 5).We performed a retrospective study on a clinical and imaging dataset of 11 children diagnosed with congenital portosystemic shunt.A total of 11 children with congenital portosystemic shunt were included in this study, 7 with extrahepatic portosystemic shunts and 4 with intrahepatic portosystemic shunts. Six patients with gastrointestinal bleeding had an extrahepatic portosystemic shunt, and the imaging results showed that the shunts originated from the splenomesenteric junction (n = 5) or splenic vein (n = 1) and connected to the internal iliac vein. Among the five cases of congenital portosystemic shunt without gastrointestinal bleeding, one case was an extrahepatic portosystemic shunt and the other four were intrahepatic portosystemic shunts.Most congenital portosystemic shunt patients with gastrointestinal bleeding had a shunt that drained portal blood into the iliac vein via an inferior mesenteric vein. This type of shunt was uncommon, but the concomitant rate of gastrointestinal bleeding with this type of shunt was high.