An autopsy case of systemic hemangiomatosis with honeycomb-like liver and focal splenic sarcomatoid changes.
An autopsy case of systemic hemangiomatosis with honeycomb-like liver and focal splenic sarcomatoid changes.
复制标题
全身性血管瘤病尸检一例，伴有肝脏蜂窝状和局灶性脾肉瘤样改变。
DOI：
10.2169/internalmedicine.37.847
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发表时间：
1998
影响因子：
1.2
通讯作者：
J. Aoki
中科院分区：
文献类型：
--
作者：
H. Tsukagoshi;Y. Iwasaki;M. Toyoda;T. Sato;H. Takagi;M. Mori;A. Sasaki;H. Kumakura;H. Ishijima;J. Aoki
一个不寻常的尸检情况下，全身性血管瘤病与蜂窝状肝脏和脾脏肉瘤样变化。患者患有继发于肝动静脉分流的高输出量室性心力衰竭伴肝功能衰竭，由于弥散性血管内凝血和肺出血而死亡。尸检显示血管形成性肿瘤在造血系统（包括肝脏、骨髓和脾脏）中的特征性分布，肝脏呈特征性蜂窝状。虽然这些血管形成性肿瘤大多数是良性的，但在脾脏病变中观察到部分肉瘤样变化。
An unusual autopsy case of systemic hemangiomatosis associated with honeycomb-like liver and splenic sarcomatoid changes is presented. The patient suffered from high-output ventricular heart failure secondary to hepatic arteriovenous shunting with hepatic failure, ending fatally due to disseminated intravascular coagulation and pulmonary bleeding. Postmortem examination revealed the characteristic distribution of vasoformative tumors presenting in the hematopoietic system including the liver, bone marrow, and spleen, with the liver appearing characteristically honeycomb-like. While these vasoformative tumors were mostly benign-appearing, partial shifts toward sarcomatoid change were observed in the splenic lesions.