Mitral Valve Replacement and Hunter Syndrome: Case Report
Mitral Valve Replacement and Hunter Syndrome: Case Report
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DOI：
10.1532/hsf98.20081108
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发表时间：
2009-02-01
影响因子：
0.6
通讯作者：
Alivizatos, P.
中科院分区：
文献类型：
--
作者：
Antoniou, Theophani;Kirvassilis, G.;Alivizatos, P.
我们报告一例罕见的继发于Hunter综合征的二尖瓣狭窄，一名33岁的男性，粘多糖样沉积症（MPS）II型。MPS患者的解剖结构异常在心脏手术中存在麻醉和手术挑战。这名特殊患者的管理因口腔分泌物过多和房颤而复杂化。通过详细的术前评估和气道管理计划，该患者成功接受了二尖瓣置换术，住院过程简单。随访6个月后，患者病情稳定。
We report a rare case of mitral valve stenosis secondary to Hunter syndrome, mucopolysaccharoidosis (MPS) type II in a 33-year-old man. Anatomical abnormalities in patients with MPS present anesthetic and surgical challenges during cardiac surgery. Management of this particular patient was complicated by excessive oral secretions and atrial fibrillation. With a detailed preoperative assessment and planning for airway management, this patient successfully underwent mitral valve replacement and had an uncomplicated hospital course. After 6 months of follow-up, the patient was still in stable condition.