Multimodality lymphatic imaging of postoperative chylothorax in an infant with Noonan syndrome: a case report.
Multimodality lymphatic imaging of postoperative chylothorax in an infant with Noonan syndrome: a case report.
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努南综合征婴儿术后乳糜胸的多模态淋巴显像：病例报告。
DOI：
10.1186/s40001-020-00455-w
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发表时间：
2020-11-04
影响因子：
4.2
通讯作者：
Aldrich MB
中科院分区：
文献类型：
--
作者：
Pham KT;Balaguru D;Tammisetti VS;Guevara CJ;Rasmussen JC;Zvavanjanja RC;Hanfland R;Sevick-Muraca EM;Aldrich MB
乳糜胸是儿科心脏手术的一种罕见并发症，更常见于努南综合征患儿，努南综合征是一种与心脏缺陷和淋巴异常相关的遗传性疾病。我们报告一例术后乳糜胸的6个月大的婴儿努南综合征，其中多模态淋巴成像引导下的管理。在近红外荧光淋巴成像（NIRFLI）过程中，下肢和上肢毛细淋巴管的引流模式被可视化。动态磁共振淋巴管造影术（MRL）进一步确定了胸导管泄漏部位，随后引导手术干预。多模态成像的应用允许更大的个体化治疗，并应考虑在复杂的情况下，如那些与乳糜胸的发病率较高的综合征的患者。IRB编号：HSC-MS-13-0754，2013年12月10日
Chylothorax is a rare complication of pediatric cardiac operations that occurs more frequently in children with Noonan syndrome, a genetic disorder associated with cardiac defects and lymphatic anomalies. We report a case of postoperative chylothorax in a 6-month-old infant with Noonan syndrome where multimodality lymphatic imaging guided management was followed. Drainage patterns of the lymphatic capillaries in the lower and upper extremities were visualized during near-infrared fluorescence lymphatic imaging (NIRFLI). Dynamic magnetic resonance lymphangiography (MRL) further identified the site of leakage in the thoracic duct and subsequently guided surgical intervention. Application of multimodality imaging allows for greater individualization of treatment and should be considered in patients with complex cases such as those with syndromes associated with a higher incidence of chylothorax. IRB Number: HSC-MS-13–0754, December 10, 2013
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影响因子：
5
作者：
Rasmussen, John C.;Tan, I-Chih;Sevick-Muraca, Eva M.
通讯作者：
Sevick-Muraca, Eva M.
影响因子：
8.8
作者：
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Zenker, M.
影响因子：
1.8
作者：
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通讯作者：
Sersar, Sameh Ibrahim
影响因子：
5.2
作者：
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通讯作者：
Mansour, Sahar
影响因子：
168.9
作者：
Roberts, Amy E.;Allanson, Judith E.;Gelb, Bruce D.
通讯作者：
Gelb, Bruce D.