Huge mesenteric fibromatosis presenting with intestinal perforation and acute diffuse peritonitis: a case report.
Huge mesenteric fibromatosis presenting with intestinal perforation and acute diffuse peritonitis: a case report.
复制标题
伴有肠穿孔和急性弥漫性腹膜炎的巨大肠系膜纤维瘤病：病例报告。
DOI：
10.21037/tcr-19-1151
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发表时间：
2020-09
影响因子：
0.9
通讯作者：
Zong L
中科院分区：
文献类型：
--
作者：
Xu Y;Duan Z;Hu W;Zhu K;You J;Abe M;Chen P;Zhang Q;Zong L
肠系膜纤维瘤病是一种局部浸润性肌纤维母细胞增生，很少转移到其他器官。肠系膜纤维瘤病引起的中空器官穿孔和急性弥漫性腹膜炎很少发生。我们报告一个以阵发性上腹痛为主诉的巨大肠系膜纤维瘤病病例，其电脑断层扫描显示有一巨大肿块、腹腔积气及腹水。一个紧急剖腹手术显示一个腹内肿块和穿孔位于空肠。术后组织学证实为肠系膜纤维瘤病。随访1年，患者无复发。我们希望分享我们的治疗经验，因为它不属于典型的类型，但表现为急性弥漫性腹膜炎，全切除和R0边缘是治疗急性病例的关键。这一非典型的病例至今未见文献报道。
Mesenteric fibromatosis is a locally invasive myofibroblastic proliferation and rarely metastasize to other organs. Hollow organ perforation and acute diffuse peritonitis caused by mesenteric fibromatosis rarely occurred. Here we report a case of huge mesenteric fibromatosis who complained a paroxysmal epigastric pain, and CT scan showed a huge mass, pneumoperitoneum and ascites. An urgent laparotomy showed an intro-abdominal mass and perforation locating at the jejunum. Postoperative histology confirmed it to be mesenteric fibromatosis. With one-year follow-up, the patient had no recurrence. We wish to share our treating experience of this interesting case because it did not belong to a typical type but presenting with acute diffuse peritonitis, and total resection and R0 margin is a key to treat acute case. This atypical one has not been reported in the literature till now.
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DOI：
10.1016/j.ijrobp.2004.07.705
发表时间：
2005-03-01
影响因子：
7
作者：
Micke, O;Seegenschmiedt, MH
通讯作者：
Seegenschmiedt, MH
影响因子：
8.4
作者：
Kasper, B.;Baumgarten, C.;Gronchi, A.
通讯作者：
Gronchi, A.
影响因子：
5.6
作者：
BURKE, AP;SOBIN, LH;HELWIG, EB
通讯作者：
HELWIG, EB
影响因子：
2.4
作者：
Al Jadaan, SA;Al Rabeeah, A
通讯作者：
Al Rabeeah, A
影响因子：
45.3
作者：
Lev, Dina;Kotilingam, Dhanasekaran;Pollock, Raphael E.
通讯作者：
Pollock, Raphael E.