Congenital anomalies causing hemato/hydrocolpos: imaging findings, treatments, and outcomes.

Congenital anomalies causing hemato/hydrocolpos: imaging findings, treatments, and outcomes.
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DOI:
10.1007/s11604-021-01115-7
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发表时间:
2021-08
影响因子:
2.1
通讯作者:
Ohtsu K
Ohtsu K
中科院分区:
医学4区
文献类型:
--
作者:
Tanitame K;Tanitame N;Urayama S;Ohtsu K

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先天性泌尿生殖系统异常引起的出血/积水是在新生儿、婴儿和青春期女孩中罕见的情况。由于其罕见的发病率和非特异性症状,常常被漏诊或延误诊断。如果不能进行早期正确的诊断和治疗,可能会出现输卵管粘连、盆腔子宫内膜异位症和不孕症等晚期并发症。先天性泌尿生殖系统异常引起的出血/积水主要有四种类型:处女膜闭锁、阴道远端发育不全、阴道横隔、半阴道闭塞和同侧肾异常,临床医生应对这些异常有足够的认识。本文旨在通过描述胚胎学、临床表现、影像表现、手术治疗和术后结果来回顾这些泌尿生殖系统畸形的诊断和治疗。
Hemato/hydrocolpos due to congenital urogenital anomalies are rare conditions discovered in neonatal, infant, and adolescent girls. Diagnosis is often missed or delayed owing to its rare incidence and nonspecific symptoms. If early correct diagnosis and treatment cannot be performed, late complications such as tubal adhesion, pelvic endometriosis, and infertility may develop. Congenital urogenital anomalies causing hemato/hydrocolpos are mainly of four types: imperforate hymen, distal vaginal agenesis, transverse vaginal septum, and obstructed hemivagina and ipsilateral renal anomaly, and clinicians should have adequate knowledge about these anomalies. This article aimed to review the diagnosis and treatment of these urogenital anomalies by describing embryology, clinical presentation, imaging findings, surgical management, and postoperative outcomes.
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