LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
批准号:
2137754
负责人:
JESS G THOENE
金额:
$20.6万
依托单位国家:
美国
项目类别:
财政年份:
1979
资助国家:
美国
项目状态:
已结题
起止时间:
1979-01-01 至 1996-12-31
期刊论文(11)
专著(0)
科研奖励(0)
会议论文
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Protein microinjection by protease permeabilization of fibroblasts.
通过成纤维细胞的蛋白酶透化进行蛋白质显微注射。
DOI:
10.1016/0003-2697(88)90435-6
发表时间:
1988
期刊:
Analytical biochemistry
影响因子:
2.9
作者:
[Lemons,R, Forster,S, Thoene,J]
通讯作者:
Thoene,J
Evidence for inhibition of exodus of small neutral amino acids from non-brain tissues in hyperphenylalaninaemic rats.
抑制高苯丙氨酸血症大鼠非脑组织中小中性氨基酸外流的证据。
DOI:
10.1007/bf01800722
发表时间:
1989
期刊:
Journal of inherited metabolic disease
影响因子:
4.2
作者:
[deCespedes,C, Thoene,JG, Lowler,K, Christensen,HN]
通讯作者:
Christensen,HN
Characterization of carrier-mediated transport systems for small neutral amino acids in human fibroblast lysosomes.
人成纤维细胞溶酶体中小中性氨基酸载体介导的转运系统的表征。
DOI:
--
发表时间:
1987
期刊:
The Journal of biological chemistry
影响因子:
--
作者:
[Pisoni,RL, Flickinger,KS, Thoene,JG, Christensen,HN]
通讯作者:
Christensen,HN
Utilization of mercaptoethylgluconamide for depleting human cystinotic fibroblasts of their accumulated lysosomal cystine.
利用巯基乙基葡糖酰胺来消耗人胱氨酸成纤维细胞中积累的溶酶体胱氨酸。
DOI:
10.1203/00006450-198907000-00020
发表时间:
1989
期刊:
Pediatric research
影响因子:
3.6
作者:
[Pisoni,RL, Lisowski,KM, Lemons,RM, Thoene,JG]
通讯作者:
Thoene,JG
Leucine and tissue distribution of bulky and small neutral amino acids in rats: dissociation between transport and insulin-mediated effects.
大鼠中亮氨酸和大中性氨基酸和小中性氨基酸的组织分布:运输和胰岛素介导作用之间的分离。
DOI:
10.1007/bf01800357
发表时间:
1992
期刊:
Journal of inherited metabolic disease
影响因子:
4.2
作者:
[deCéspedes,C, Thoene,JG, Lowler,K, Christensen,HN]
通讯作者:
Christensen,HN
共 8 条
TK019: A Study of Replagal Enzyme Replacement Therapy
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批准号:7044000
-
项目类别:
-
资助金额:$0.3万
-
财政年份:2003
-
负责人:JESS G THOENE
-
依托单位:
NTBC THERAPY OF TYROSINEMIA TYPE I
-
批准号:6297102
-
项目类别:
-
资助金额:$0.02万
-
财政年份:1998
-
负责人:JESS G THOENE
-
依托单位:
AMINOTHIOL THERAPY IN NEPHROPATHIC CYSTINOSIS
-
批准号:6297099
-
项目类别:
-
资助金额:$0.02万
-
财政年份:1998
-
负责人:JESS G THOENE
-
依托单位:
NTBC THERAPY OF TYROSINEMIA TYPE I
-
批准号:6113393
-
项目类别:
-
资助金额:$0.02万
-
财政年份:1998
-
负责人:JESS G THOENE
-
依托单位:
AMINOTHIOL THERAPY IN NEPHROPATHIC CYSTINOSIS
-
批准号:6113426
-
项目类别:
-
资助金额:$0.02万
-
财政年份:1998
-
负责人:JESS G THOENE
-
依托单位:
AMINOTHIOL THERAPY IN NEPHROPATHIC CYSTINOSIS
-
批准号:6274660
-
项目类别:
-
资助金额:$2.15万
-
财政年份:1997
-
负责人:JESS G THOENE
-
依托单位:
NTBC THERAPY OF TYROSINEMIA TYPE I
-
批准号:6274627
-
项目类别:
-
资助金额:$2.15万
-
财政年份:1997
-
负责人:JESS G THOENE
-
依托单位:
AMINOTHIOL THERAPY IN NEPHROPATHIC CYSTINOSIS
-
批准号:6244626
-
项目类别:
-
资助金额:$2.22万
-
财政年份:1997
-
负责人:JESS G THOENE
-
依托单位:
STUDY AND TREATMENT OF INBORN ERROR OF METABOLISM
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批准号:6274723
-
项目类别:
-
资助金额:$2.15万
-
财政年份:1997
-
负责人:JESS G THOENE
-
依托单位:
NTBC THERAPY OF TYROSINEMIA TYPE I
-
批准号:6244584
-
项目类别:
-
资助金额:$2.22万
-
财政年份:1997
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:2137753
-
项目类别:
-
资助金额:$19.82万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
PROTEIN DEGRADATION IN INFANTILE NEPHROPATHIC CYSTINOSIS
-
批准号:3151518
-
项目类别:
-
资助金额:$6.31万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227485
-
项目类别:
-
资助金额:$19.06万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227479
-
项目类别:
-
资助金额:$15.68万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227477
-
项目类别:
-
资助金额:$13.77万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227483
-
项目类别:
-
资助金额:$13.27万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227482
-
项目类别:
-
资助金额:$12.14万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227480
-
项目类别:
-
资助金额:$2.76万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
LYSOSOMAL PHYSIOLOGY & PROTEIN DEGRADATION IN CYSTINOSIS
-
批准号:3227484
-
项目类别:
-
资助金额:$18.85万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
PROTEIN DEGRADATION IN INFANTILE NEPHROPATHIC CYSTINOSIS
-
批准号:3227481
-
项目类别:
-
资助金额:$6.86万
-
财政年份:1979
-
负责人:JESS G THOENE
-
依托单位:
海外基金