ROSS LABORATORIES MULTIPLE INVESTIGATOR STUDY OF GROWTH TOLERANCE AND PLASMA

尽管对L-氨基酸混合物有合理的临床经验 苯丙酮尿症的治疗，L-氨基酸是 约75%的膳食蛋白质当量的来源 目前还没有系统的研究来确定它们的有效性 在支持长期增长和维持正常氨基酸方面 配置文件。这项研究是对L-氨基能力的一次尝试 酸混合物，如罗斯代谢式体系(RMFS)的混合物 支持PKU患儿的正常营养状态。

Despite reasonable clinical experience with mixtures of L-amino acids in the management of Phenylketonuria (PKU), L-amino acids which are the source of approximately 75% of dietary protein equivalent in this condition have not been systematically studied to determine their efficacy in supporting longterm growth and in maintaining normal amino acid profiles. This study is an attempt to evaluate the ability of L-amino acid mixtures such as that of the Ross Metabolic Formula System (RMFS) to support normal nutritional status of infants with PKU.