EPHEDRINE AND LOW CARBOHYDRATE DIET FOR LATE ONSET ACID MALTASE DEFICIENCY
EPHEDRINE AND LOW CARBOHYDRATE DIET FOR LATE ONSET ACID MALTASE DEFICIENCY
批准号:
6246875
负责人:
Frank T Martiniuk
金额:
$2.39万
依托单位国家:
美国
项目类别:
财政年份:
1997
资助国家:
美国
项目状态:
已结题
起止时间:
1997-02-12 至 1997-11-30
关键词:
clinical research clinical trials diet therapy dietary carbohydrates drug screening /evaluation electromyography ephedrine exercise glycogen storage disease type II human subject human therapy evaluation metabolism disorder chemotherapy muscle function muscle strength nutrition related tag respiratory function
中文摘要
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英文摘要
The aims of this protocol are to determine the clinical, biochemical,
muscle strength, muscle function, pulmonary function, EMG, and molecular
genetic status of acid maltase deficiency patients. Interventions such as
low carbohydrate diet, moderate daily exercise, and daily oral ephedrine
therapy will be assessed at designated intervals.
期刊论文(0)
专著(0)
科研奖励(0)
会议论文
GLYCOGENOSIS TYPE II--MOLECULAR ANALYSIS OF PATIENTS
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批准号:6305971
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项目类别:
-
资助金额:$2.1万
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财政年份:1999
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负责人:Frank T Martiniuk
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依托单位:
NOVEL MUSCLE SPECIFIC VECTOR FOR GENE THERAPY OF ACID MALTASE DEFICIENCY
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批准号:6305917
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项目类别:
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资助金额:$2.1万
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财政年份:1999
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负责人:Frank T Martiniuk
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依托单位:
NOVEL MUSCLE SPECIFIC VECTOR FOR GENE THERAPY OF ACID MALTASE DEFICIENCY
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批准号:6115802
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项目类别:
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资助金额:$2.1万
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财政年份:1998
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负责人:Frank T Martiniuk
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依托单位:
GLYCOGENOSIS TYPE II--MOLECULAR ANALYSIS OF PATIENTS
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批准号:6115834
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项目类别:
-
资助金额:$2.1万
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财政年份:1998
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负责人:Frank T Martiniuk
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依托单位:
MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:6246899
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项目类别:
-
资助金额:$2.39万
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财政年份:1997
-
负责人:Frank T Martiniuk
-
依托单位:
NOVEL MUSCLE SPECIFIC VECTOR FOR GENE THERAPY OF ACID MALTASE DEFICIENCY
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批准号:6277036
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项目类别:
-
资助金额:$2.03万
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财政年份:1997
-
负责人:Frank T Martiniuk
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依托单位:
GLYCOGENOSIS TYPE II--MOLECULAR ANALYSIS OF PATIENTS
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批准号:6277068
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项目类别:
-
资助金额:$2.03万
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财政年份:1997
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负责人:Frank T Martiniuk
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依托单位:
MECHANISM OF INH AND RIFAMPICIN RESISTANCE IN TB
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批准号:2228323
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项目类别:
-
资助金额:$21.62万
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财政年份:1994
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负责人:Frank T Martiniuk
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依托单位:
MECHANISM OF INH AND RIFAMPICIN RESISTANCE IN TB
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批准号:2228324
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项目类别:
-
资助金额:$23.91万
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财政年份:1994
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负责人:Frank T Martiniuk
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依托单位:
MECHANISM OF INH AND RIFAMPICIN RESISTANCE IN TB
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批准号:2460035
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项目类别:
-
资助金额:$24.87万
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财政年份:1994
-
负责人:Frank T Martiniuk
-
依托单位:
MECHANISM OF INH AND RIFAMPICIN RESISTANCE IN TB
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批准号:2228322
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项目类别:
-
资助金额:$20.61万
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财政年份:1994
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负责人:Frank T Martiniuk
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依托单位:
THE MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:3239542
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项目类别:
-
资助金额:$11.41万
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财政年份:1988
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负责人:Frank T Martiniuk
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依托单位:
THE MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:3239543
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项目类别:
-
资助金额:$11.22万
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财政年份:1988
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负责人:Frank T Martiniuk
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依托单位:
THE MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:3239544
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项目类别:
-
资助金额:$11.11万
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财政年份:1988
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负责人:Frank T Martiniuk
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依托单位:
MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:3239537
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项目类别:
-
资助金额:$11.75万
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财政年份:1988
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负责人:Frank T Martiniuk
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依托单位:
THE MOLECULAR BIOLOGY OF ACID MALTASE DEFICIENCY
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批准号:2140290
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项目类别:
-
资助金额:$5.88万
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财政年份:1986
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负责人:Frank T Martiniuk
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依托单位:
海外基金