Ileocecal ulcers accompanied by relapsing polychondritis: a case report.
Ileocecal ulcers accompanied by relapsing polychondritis: a case report.
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DOI：
10.1186/2193-1801-3-714
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发表时间：
2014
期刊：
影响因子：
--
通讯作者：
Shimosegawa T
中科院分区：
文献类型：
--
作者：
Kawakami Y;Endo K;Ishii T;Haneda S;Fujishima F;Kakuta Y;Shiga H;Kinouchi Y;Shimosegawa T
口腔和生殖器溃疡伴炎症软骨（MAGIC）综合征是一种罕见的重叠综合征，包括白塞氏病（BD）和复发性息肉病（RP）的特征。一名30岁女性主诉在RP治疗期间出现下腹疼痛和血便。全结肠镜检查显示回肠末端椭圆形深溃疡，与肠BD相似。在进行回盲部切除术后，RP和胃肠道病变均复发，但经英夫利西单抗治疗后有所改善。在RP的药物治疗过程中，我们经历了一个罕见的回盲部溃疡病例，类似于肠BD。虽然我们的病例因为缺乏BD的主要临床症状而不符合肠BD的诊断标准，但肠病变与肠BD有着非常相似的特征。我们的病例可能是一种罕见的MAGIC综合征亚型，具有肠道BD和RP的特征。我们报告一个罕见的回盲部溃疡病例，没有任何BD症状，但伴有RP，可能是MAGIC综合征的一个亚型。本文的在线版本（doi：10.1186/2193-1801-3-714）包含补充材料，可供授权用户使用。
Mouth and genital ulcers with inflamed cartilage (MAGIC) syndrome is a rare overlap syndrome that includes features characteristic of both Behçet’s disease (BD) and relapsing polychondritis (RP). A 30-year-old female complained of lower abdominal pain and bloody stools during medical treatment for RP. Total colonoscopy revealed oval-shaped deep ulcers on the terminal ileum similar to those of intestinal BD. After performing the ileocecal resection, both RP and gastrointestinal lesions relapsed, but improved with infliximab treatment. During medical treatment for RP, we experienced a rare case with ileocecal ulcers similar to intestinal BD. Although our case did not meet the diagnosis criteria of intestinal BD because of the lack of BD’s major clinical symptoms, intestinal lesions shared quite similar features with intestinal BD. Our case could possibly be a rare subtype of MAGIC syndrome that had the features characteristic of both intestinal BD and RP. We described a rare case of ileocecal ulcers without any BD symptoms but accompanied by RP, possibly be a subtype of MAGIC syndrome. The online version of this article (doi:10.1186/2193-1801-3-714) contains supplementary material, which is available to authorized users.
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