EFFECT OF FEEDING, EXERCISE AND GENOTYPE ON PLASMA 3-HYDROXYACYLCARNITINES IN CHILDREN WITH LCHAD DEFICIENCY.
EFFECT OF FEEDING, EXERCISE AND GENOTYPE ON PLASMA 3-HYDROXYACYLCARNITINES IN CHILDREN WITH LCHAD DEFICIENCY.
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喂养、运动和基因型对 LCHAD 缺乏儿童血浆 3-羟基肉碱的影响。
DOI：
10.1097/tin.0b013e3181c62182
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发表时间：
2009
影响因子：
0.5
通讯作者：
Harding,CaryO
中科院分区：
文献类型：
--
作者：
Gillingham,MelanieB;Matern,Dietrich;Harding,CaryO
Chronic complications observed in patients with long-chain 3-hydroxyacyl coenzyme A dehydrogenase (LCHAD) or trifunctional protein (TFP) deficiency may be mediated by the accumulation of 3-hydroxy fatty acid compounds. To understand variation in metabolite accumulation, 3-hydroxyacylcarnitine concentrations were measured by tandem mass spectrometry before and after a mixed meal and moderate-intensity exercise. Subjects who were homozygous or heterozygous for the common mutation (c. 1528G> C) in the TFP alpha subunit (LCHAD deficiency) had significantly higher 3-hydroxyacylcarnitines than subjects with TFP deficiency. Feeding a mixed meal significantly suppressed and exercise significantly increased plasma 3-hydroxyacylcarnitines concentrations.
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前列环素是从离体灌注兔和大鼠心脏中释放的主要前列腺素
影响因子：
64.8
作者：
E. A. de Deckere;D. Nugteren;F. TEN HOOR
通讯作者：
F. TEN HOOR
采用电化学检测的高效液相色谱法测定血浆儿茶酚胺：与放射性酶法的比较。
影响因子：
6.1
作者：
P. Hjemdahl;M. Daleskog;T. Kahan
通讯作者：
T. Kahan
DOI：
--
发表时间：
1979
期刊：
Acta Physiologica Scandinavica
影响因子：
--
作者：
B. Fredholm;P. Hedqvist;L. Vernet
通讯作者：
L. Vernet
影响因子：
--
作者：
JACOB, MI;BERNE, RM
通讯作者：
BERNE, RM
DOI：
10.1111/j.1748-1716.1982.tb07142.x
发表时间：
1982-01-01
期刊：
ACTA PHYSIOLOGICA SCANDINAVICA
影响因子：
--
作者：
FREDHOLM, BB;HEDQVIST, P;WENNMALM, M
通讯作者：
WENNMALM, M