GLYCOGEN STORAGE DISEASE

这项研究的目的是测试不同的反应 不同类型葡萄糖-6-磷酸酶缺乏症患者 喂食生淀粉时葡萄糖的水解和吸收 来自不同的来源。当得到发散的结果时， 他们继续进行家庭研究。此外，所获得的结果是 供应给管理中的患者的葡萄糖6 磷酸酶缺乏症。 使用经过测试的煮熟和未煮熟的淀粉 体内，我们测定了淀粉酶的体外煮熟和 使用商业淀粉酶和患者血清的生淀粉。 我们没有看到体内和体外结果之间存在1：1的相关性 预期中。

The study is designed to test the heterogeneous responses of different patients with glucose 6 phosphatase deficiency in hydrolyzing and absorbing glucose when administered raw starches from different sources. When divergent results are obtained, family studies are pursued. Further, the results obtained are supplied to the management of the patients with glucose 6 phosphatase deficiency. Using cooked and uncooked starches which have been tested in vivo, we have measured amylase in vitro with cooked and uncooked starches using commercial amylase and patients sera. We did not see the 1:1 correlation of in vivo and in vitro results expected.