GLYCOGEN STORAGE DISEASE

该研究旨在测试不同的异质性反应， 葡萄糖6磷酸酶水解和吸收缺陷患者 葡萄糖时给予生淀粉从不同来源。 当 得到了不同的结果，家庭研究被说服。 此夕h 所得结果应用于血糖患者的管理 6磷酸酶缺乏症。 正在尝试将各种淀粉掺入到 丙烯酰胺凝胶，然后确定是否可以显示异质性 使用病人的血清

The study is designed to test the heterogeneous responses of different patients with glucose 6 phosphatase deficiency in hydrolyzing and absorbing glucose when administered raw starches from different sources. When divergent results are obtained, family studies are persued. Further, the results obtained are applied to the management of the patients with glucose 6 phosphatase deficiency. Attempts are underway attempting to incorporate the various starches into acrylamide gels and then determine whether the heterogeneity can be shown using serum from the patients.